Hemolytic anemia - a rare hereditary disease

In most cases, hemolytic anemia is a hereditary disease, fortunately, quite rare.For example, in Europe the frequency of anemia defined as 1 : 5000.

Given this fact, it turns out that patients generally are aware of their disease since birth.But we must remember that in a quarter of cases, even with careful study of the parents of a sick child can not find any changes in the blood picture, so that at the beginning of the doctors without getting lost family history, suspecting other diseases.

There are hereditary and acquired anemia.

acquisition, which is in turn divided into:

  • immune,
  • Autoimmune,
  • Idiopathic.

Signs and causes of the disease

Acquired hemolytic anemia may result from ingestion of poisons, after burns, in the application of certain drugs, and transfusion of incompatible blood.

Anemia in infants related to immune deficiency anemia, which occurs in the case of Rh-conflict with the mother's blood.

have autoimmune anemia reason - lymphocytic leukemia, systemic diseases, ma

laria, infection, sepsis.

causes are not known in idiopathic anemias.In this case we speak about the possible precipitating factors: pregnancy and childbirth, trauma, acute viral infection.

Cause of hereditary anemias - genetics.

Symptoms

diseases Now let's talk about the most important section in the structure of any disease - about the symptoms.If you do not take into account the hereditary anemia, in all other cases, you must immediately recognize the symptoms of anemia, as shown in an emergency intervention.Therefore, first, consider the hospital acquired anemias.

1.Anemiya infants.This anemia can occur if a mother and the fetus does not coincide or Rh blood group.

  • edema, is the most rare form, and the baby often dies in the womb or in the first hours after birth.
  • Mild anemia without jaundice - the most favorable option.
  • And the most common form - hemolytic anemia in children: a pronounced anemia and jaundice in the blood.This form is dangerous because it is not immediately recognizable.Often such anemia developed in a few days, and symptoms appear when the hemoglobin level dropped to critical.

Probably, it is necessary to immediately respond to the following question: "What is the treatment of anemia?" Treatment exists, so that young parents should not panic.It is necessary to make the babies blood transfusions.This must be done in the first days after birth, which is the case with the third embodiment is quite problematic.

Breastfeeding is canceled, so that either artificial or need to use milk nurse.

2. Symptoms of autoimmune and idiopathic anemia are very similar.This hemolytic anemia can occur in the background of "overall health".



Most often it develops in frail elderly people.Patients may complain of not characteristic symptoms of anemia: weakness, shortness of breath, back pain, heart, joints.It turns out that the anemia can be disguised as other diseases.Jaundice may not be, so should be alert to anemia if there is a corresponding history.

3.BASIC symptom of hereditary anemias - jaundice.In the future spine deformity occurs in children, the skull has special features: square, bite changes, small eyes on the face.

for all types of anemia characterized by enlarged spleen.And, of course, the diagnosis can not be delivered without a full blood count.

Therapies hemolytic anemia

We've already talked a little about the treatment section - anemia in infants.The same principle is used for treatment of other types of anemia.The main method is the transfusion of blood, especially during a crisis.When hereditary anemia during adolescence do splenectomy - removal of the spleen.To prevent crises prescribe folic acid, acetylsalicylic acid.In the case of autoimmune anemia hormones necessary appointment.

In any case, with a diagnosis of hemolytic anemia children live, leading an active lifestyle, while respecting certain limits.In the case of acquired anemia must be timely identification of the disease, in this case, a favorable prognosis.So do not waste time, even if you think you know the cause of their symptoms.Only a doctor can make a diagnosis, and then spending a whole range of additional research.

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